Degos Disease

[Dowling-Degos disease].

Dowling-Degos disease.

Dowling-Degos disease (DDD) is a rare autosomal dominant inherited pigmentary disorder of the flexures with a reticulate aspect and with presence of prominent comedone-like lesions and pitted scars. The diagnosis includes acanthosis nigricans as well as other reticulate pigmentary disorders classified into: dyschromatrosis symmetrica hereditaria (DSH), dyschromatosis universalis hereditaria (DU...

Benign cutaneous Degos disease

A 41-year-old woman presented with a 2-year history of multiple asymptomatic pea-sized papules with an erythematous, telangiectatic rim surrounding an atrophic, porcelain-white center on the trunk and extremities (Figure 1). She had experienced abdominal fullness and vomiting for 1 year. Histopathologic examination of a skin biopsy from the left forearm revealed hyperkeratosis, epidermal atroph...

Degos' disease mimicking vasculitis.

Introduction Degos’ disease is a rare disorder with multisystem involvement and unknown etiology. This entity was first described by Degos in 1942 (1,2). Other synonyms for this disease are malignant atrophic papulosis, atrophic papulosquamous dermatitis, fatal cutaneous-intestinal syndrome, and thromboangiitis cutaneointestinalis disseminata (3). It has been more commonly reported in whites, m...

Degos Disease Associated with Behçet's Disease

Vol. 27, No. 2, 2015 235 Received March 13, 2014, Revised May 14, 2014, Accepted for publication June 23, 2014 Corresponding author: Jee-Bum Lee, Department of Dermatology, Chonnam National University Hospital, 42 Jebong-ro, Dong-gu, Gwangju 501-757, Korea. Tel: 82-62-220-6684, Fax: 82-62-222-4058, E-mail: [email protected] This is an Open Access article distributed under the terms of the Creati...